Home | Register | Login | Inquiries | Alerts | Sitemap |  

Advanced Search
J Korean Acad Pediatr Dent. 2011;38(1): 56-61.
CORNELIA DE LANGE SYNDROME: A CASE REPORT
Eun-Joo Choi, Hong-Keun Hyun, Young-Jae Kim, Jung-Wook Kim, Sang-Hoon Lee, Chong-Chul Kim, Se-Hyun Hahn, Ki-Taeg Jang
Department of Pediatric Dentistry, School of Dentistry, Seoul National University
Corresponding Author: Ki-Taeg Jang ,Tel: 02-2072-2682, Email: jangkt@snu.ac.kr
Received: October 5, 2010;  Accepted: December 15, 2010.
Share :  
ABSTRACT
Cornelia de Lange syndrome(CdLS) is a well-described multiple malformation syndrome typically involving proportionate small stature, developmental delay, specific facial features, major malformations, and behavioral abnormalities. Dental issues include micrognathia, crowding of teeth, small teeth, absent teeth, poor oral hygiene, and periodontal disease. We present a case of CdLS in a 10-year-old girl. Micrognathia, crowding of teeth, and bifid uvula are the characteristic features of this case. Dental treatments for this child including preventive and restorative procedures were performed under outpatient general anesthesia.
Keywords: Cornelia de Lange syndrome | Dental problem | General anesthesia
Editorial Office
Seoul National University, Dental Hospital, B1-166 101, Daehak-ro, Jongno-gu, Seoul, 110-744
Tel. +82-70-4145-8875,    Fax. +82-2-745-8875   E-mail : info@kapd.org

Copyright© Korean Academy of Pediatric Dentistry. All right reserved.                powerd by m2community
About |  Browse Articles |  Current Issue |  For Authors and Reviewers