AMELOGENESIS IMPERFECTA : REPORT OF CASE

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Journal of the Korean Academy of Pediatric Dentistry 1998;25(3):598-603.
Published online August 31, 1998.

AMELOGENESIS IMPERFECTA : REPORT OF CASE

법랑질 형성 부전증에 관한 증례 보고

김재곤, 이영수, 허선, 박종하, 백병주

전북대학교 치과대학 소아치과학교실 및 치의학연구소

Abstract

Amelogenesis imperfecta is a group of hereditary defects of enamel unassociated with any other generalized defects. The prevalence of this condition has been estimated to range from 1 in 14,000 to 1 in 16,000, depending on the population studied. It may be differentiated into three general types : hypoplastic, hypocalcified, and hypomaturation, depending on the clinical presentation of the defects and the likely stage of enamel formation that is primarily affected. The dentin and root form are usually normal, but the enamel may lack the normal prismatic structure, being laminated throughout its thickness or at the periphery, with the result that these teeth are more resistant to decay. This case is that of an six-year-old girl brought to the pediatric dentistry department by her parents for esthetic reasons and also because of slight dental sensitivity. Clinical and radiographic examinations confirmed amelogenesis imperfecta. The author has treated with the crowning of the primary molars, using prefomed NiCr crowns and periodic fluoride application on whole dentition.

Key Words: amelogenesis imperfecta, hereditary defects, hypocalcified, hypomaturation, hypoplastic