Journal of the Korean Academy of Pediatric Dentistry 2009;36(1):145-149.
Published online February 28, 2009.
STURGE-WEBER SYNDROME : A CASE REPORT
Hye-Sung Shin, Kyu-ho Yang, Nam-ki Choi, Seon-mi Kim
Department of Pediatric Dentistry, Chonnam National University School of Dentistry, Dental Research Institute and Second stage of BK21 
Correspondence:  Seon-mi Kim,  Tel: 062-530-5668, Email: hellopedo@hanmail.net
Received: 16 May 2008   • Accepted: 12 December 2008
Abstract
Sturge-Weber Syndrome is a rare congenital disorder and is characterized by port wine nevus following one or more divisions of trigeminal nerve, ocular involvement(eg, glaucoma) and neurologic involvement(eg, epilepsy, mental retardation). Oral menifestations include unilateral blood vessel expansion of the oral mucosa and gingiva, gingival hyperplasia, giant tooth, ipsilateral large tongue, blood vessel anomaly of maxilla or mandible and abnormal eruption sequence. This case report is about 8-year-old Sturge-Weber Syndrome patient presented violet discoloration on upper gingiva and buccal mucosa, gingival hyperplasia and abnormal eruption sequence. In this case, we performed lingual frenectomy and periodic oral hygiene management, and obtained satisfactory result.
Key Words: Sturge-Weber Syndrome, Lingual frenectomy, Port wine nevus


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