GINGIVAL HYPERPLASIA IN A MUCOPOLYSACCHARIDOSIS' PATIENT : A CASE REPORT |
서울대학교 치과대학 소아치과학교실 및 치의학연구소 |
뮤코다당증(Mucopolysaccharidosis)환아의 치은 증식 |
송주현, 장철호, 김영재, 한세현, 이상훈 |
서울대학교 치과대학 소아치과학교실 및 치의학연구소 |
Correspondence:
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Abstract |
Mucopolysaccharidosis (MPS) is a disorder of storage in which there is excessive accumulation of glycosaminoglycans (GAGs) from lysosomal enzyme defect. Lysosomal accumulation of GAGs eventually results in cell, tissue and organ dysfunction. This patient may manifest mental retardation and physical disorders. This clinical report presents a girl with MPS having severe gingival hyperplasia. Gingivectomy was performed under general anesthesia. The pediatric dentist must be aware of oral manifestations present in the MPS. The approach to dental management will require teamwork between the dentist and the patient's physician. |
Key Words:
Mucopolysaccharidosis, Gingival hyperplasia, Gingivectomy |
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