DENTAL TREATMENTS OF THE CHILD WITH LOWE SYNDROME : A CASE REPORT

Ju, Chan-Hee; Kim, Seon-Mi; Choi, Nam-Ki

Journal of the Korean Academy of Pediatric Dentistry 2012;39(2):161-165.
Published online May 31, 2012.

DENTAL TREATMENTS OF THE CHILD WITH LOWE SYNDROME : A CASE REPORT

Chan-Hee Ju, Seon-Mi Kim, Nam-Ki Choi

Department of Pediatric Dentistry, School of Dentistry, Chonnam National University

Lowe syndrome 환아의 치과적 치료 : 증례보고

주찬희, 김선미, 최남기

전남대학교 치의학전문대학원 소아치과학교실

Correspondence: Nam-Ki Choi, Tel: 062-530-5668, Email: nkchoi@chonnam.ac.kr

Received: 2 August 2011 • Accepted: 20 September 2011

Abstract

Lowe syndrome, also known as oculocerebrorenal syndrome, is a rare genetic disorder involving eyes, kidney, brain and musculoskeletal system, and occurs predominantly in males. The patient with Lowe syndrome is characterized with congenital cataracts, glaucoma, prominent forehead, thin and sparse hair, mental and growth retardation, muscular hypotonia, renal dysfunction, and metabolic bone disease. We have experienced a 10-year-old boy with Lowe syndrome who had poor oral hygiene and trouble for teeth brushing. To manage his behavior and systemic metabolic disorder, sedation was performed during dental care. Excessive calculus formation in this patient is caused by both medication and lack of ability to maintain oral hygiene. The dental management of those patients has to be focused on prevention due to difficulties in dental treatment and dangers of general anesthesia for the Lowe syndrome.

Key Words: Lowe syndrome, Dental management, Prevention