CLEIDOCRANIAL DYSPLASIA : CASE REPORT

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Journal of the Korean Academy of Pediatric Dentistry 2004;31(3):372-380.
Published online August 31, 2004.

CLEIDOCRANIAL DYSPLASIA : CASE REPORT

쇄골두개 이형성증 환아의 증례 보고

박영옥, 김은정, 김현정, 김영진, 남순현

경북대학교 치과대학 소아치과학교실

Correspondence: ,

Abstract

Cleidocranial dysplasia(CCD) is a congenital disorder of skeletal and dental abnormality, which is mesodermal dysfunction influencing many tissues and organs. Skeletal abnormalities in CCD are delayed closure of cranial suture and fontanelle, presence of wormian bone and clavicle aplasia. And CCD has an effect on the long bones, phalanges, spine, pelvis, muscles, and central nervous system. Dental manifestations include retention of deciduous teeth, multiple supernumerary teeth, delayed or absent eruption of permanent teeth and formation of cysts around nonerupted teeth. But as a result in common with a lack of medical and physical disability patient may have no substantive complaint, there are many masticatory and psychological problem by absent eruption of permanent teeth after exfoliation of deciduous teeth. For this reason CCD is necessary fo early diagnosis and must be improvement of the patient's appearance as well as provision of a functioning masticatory mechanism by treatment of surgical removal of supernumerary teeth, followed orthodontically eruption of the natural permanent teeth at adequate time.

Key Words: Cleidocranial dysplasia, Unerupted teeth, Eruption guidance