CLEIDOCRANIAL DYSPLASIA : REPORT OF A CASE

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Journal of the Korean Academy of Pediatric Dentistry 2005;32(4):703-708.
Published online November 30, 2005.

CLEIDOCRANIAL DYSPLASIA : REPORT OF A CASE

쇄골두개 이형성증 환자에 관한 증례보고

이연호, 유승훈, 김종수

단국대학교 치과대학 소아치과학교실

Correspondence: ,

Abstract

Cleidocranial Dysplasia(CCD) is a congenital disorder of skeletal and dental anomaly with an autosomal dominant mode of inheritance. CCD Shows a generalized defect in intramembranous bones, such as the skull, clavicles, and endochondral bones, such as the long bones and the remainder of the skeleton. The specific clinical feature of CCD is an aplasia & hypoplasia of one or both clavicles, frontal & parietal bone bossing, incomplete fontanels and sutures closure of cranial bone. Generally, relative mandibular prognathism is seen, because maxillar is underdeveloped. Dental anomalies of CCD are prolonged primary teeth, delayed eruption of the permanent teeth and multiple supernumerary teeth. Almost patients of CCD can not recognize their dental abnormality until the permanent teeth eruption was begining. So it is difficult to decide the proper timing of the treatment of patients of CCD. Pedodontists should understand the development of the dentition in CCD patient and start the treatment of CCD patient in proper time.

Key Words: Cleidocranial dysptasia, Supernumerary teeth